Corneal atypical fibroxanthoma in xeroderma pigmentosum

Atypical Fibroxanthoma In a Patient with Xeroderma Pigmentosum

 SUMMARY X. Pis a rare autosomal recessive genodermatosis characteriseJ by photophohia, severe solar sensitivity, cutaneous pigmentary changes, xerosis and early Jevdopment of mucocutaneous and ocular cancer particularly in sun exposeJ skin. Tumors whichinclude solar keratosis, cutaneous horn, keratoachanthoma, squamous and basal cell carcinoma, malignant melanoma and angioma may developeJ in...

Atypical Fibroxanthoma of the Conjunctiva in Xeroderma Pigmentosum.

BACKGROUND Atypical fibroxanthoma (AFX) is a pleomorphic tumor that most commonly presents in the elderly and arises on sun-exposed skin. METHODS We report a case of a 24-year-old white male with xeroderma pigmentosum (XP), who developed an AFX of the conjunctiva, and review the literature. RESULTS The patient presented with a rapidly growing conjunctival mass which was surgically excised a...

Corneal Involvement in Xeroderma Pigmentosum;a Histopathologic Report

PURPOSE To report the histopathologic features of corneal involvement in a patient with xeroderma pigmentosum (XP). CASE REPORT A 19-year-old man with XP presented with bilateral corneal leukoma and decreased visual acuity predominatly in his right eye. Penetrating keratoplasty was performed in the right eye due to severe corneal opacity, vascularization and lipid deposition. The corneal butt...

corneal involvement in xeroderma pigmentosum: a histopathologic report

purpose: to specify histopathologic features of corneal involvement in a case with xeroderma pigmentosum (xp). case report: a 19-year-old man with a clinical diagnosis of xp presented with bilateral corneal leukoma and decreased visual acuity predominatly in his right eye. penetrating keratoplasty was performed in the right eye due to severe corneal opacity, vascularization and lipid deposition...

Xeroderma pigmentosum.